Q87.11 Prader-Willi syndrome
Instructional Notes:
-
Q87.11
Description: Prader-Willi syndrome
↓
-
Q87.1
Description: Congenital malformation syndromes predominantly associated with short stature
Exclude1:
- Ellis-van Creveld syndrome (Q77.6)
- Smith-Lemli-Opitz syndrome (E78.72)
↓
-
Q87
Description: Other specified congenital malformation syndromes affecting multiple systems
Use Additional Code:
- code(s) to identify all associated manifestations
↓
-
Q80-Q89
Description: Other congenital malformations (Q80-Q89)
↓
-
Q00-Q99
Description: Congenital malformations, deformations and chromosomal abnormalities
Exclude2:
- inborn errors of metabolism (E70-E88)
Notes:
- Codes from this chapter are not for use on maternal records